Caring for people with cystic fibrosis has changed considerably since the first description of the disorder and continues to evolve in the era of highly effective modulator therapy. These new treatment advancements are resulting in improved health outcomes…
February 2022
Remaining Barriers to Normalcy in Cystic Fibrosis VII
Increasing life expectancy in cystic fibrosis: Advances and challenges
Since the first description of cystic fibrosis in 1938, there have been significant advances in both quality of life and longevity for people living with this disease. In this article we describe the milestones of the last 80…
Health disparity in CF: Perspectives from a lived experience
In this commentary, we discuss health disparities, reflecting on our experience in delayed diagnosis of cystic fibrosis based on race and bias in healthcare practitioners. After reading this article, test your knowledge at: https://cfbarriers.com/quiz-2022/q2.
The indispensable role of pharmacy services and medication therapy management in cystic fibrosis
Care for people with cystic fibrosis (PWCF) is highly complex and requires a multidisciplinary approach where the pharmacist plays a vital role. The purpose of this manuscript is to serve as a guideline for pharmacists and pharmacy technicians…
Overweight and cystic fibrosis: An unexpected challenge
Achieving a healthy weight balance has been a central focus of care for people who have cystic fibrosis (CF). Over the years, the emphasis has primarily been on promoting weight gain to optimize pulmonary outcomes. With continued improvements…
Airway clearance and exercise for people with cystic fibrosis: Balancing longevity with life
Airway clearance has been an integral part of cystic fibrosis (CF) care for almost as long as CF has been identified as a condition. From diagnosis as a neonate through to end-of-life care, airway clearance is an everyday…
Recent advances in the early treatment of cystic fibrosis: Bridging the gap to highly effective modulator therapy
Highly effective modulator therapy (HEMT) for cystic fibrosis (CF) has been touted as one of the greatest advances to date in CF care. As these therapies are now available for many older children and adults with CF, marked…
Family-building and parenting considerations for people with cystic fibrosis
As people with cystic fibrosis (CF) live longer and healthier lives, increasing numbers are considering the full range of reproductive options for their futures, including parenthood, pregnancy, or pregnancy prevention. As the face of CF changes, the CF…
Optimizing sexual and reproductive health across the lifespan in people with cystic fibrosis
With improved therapies, people with cystic fibrosis are living longer and healthier lives and increasingly have questions surrounding their sexual and reproductive health. This article will summarize the important issues of which providers should be aware during the…
An overview of noninvasive ventilation in cystic fibrosis
Noninvasive ventilation (NIV) use was initially reported in cystic fibrosis (CF) in 1991 as a bridge to lung transplantation, and over the decades, the use of NIV has increased in the CF population. Individuals with CF are prone…