Quiz and Survey for Remaining Barriers to Normalcy in Cystic Fibrosis, Volume 7 In each question there is only one correct answer. 1. Between the initial description of cystic fibrosis in 1938 and the advent of the first CFTR modulator therapy, median predicted survival for CF in the US increased by approximately A. 5-fold B. 10-fold C. 15-fold D. 25-fold 2. Contributors to health disparities in CF may include A. Low socioeconomic status B. Practitioner implicit bias C. Inaccurate belief that CF only affects people of northern European ancestry D. All of the above 3. Integrating pharmacists into CF teams has been associated with these outcomes in people with CF EXCEPT A. Increased adherence to dornase alfa therapy B. Increased adverse drug interactions C. Increased body mass index D. Increased medication possession 4. When approaching a person with CF who is overweight or obese, clinicians should A. Use their expertise to persuade multiple changes in health behaviors to reduce body weight B. Focus on avoiding negative behaviors such as “junk food consumption” C. Seek alignment with the overweight person using motivational interviewing techniques D. Assume an adequate food supply at home 5. In people with CF, regular exercise A. Is less common than in the general population B. Is often used as a substitute for airway clearance C. Is proven to be equivalent to airway clearance D. Worsens glycemic control 6. Young children with CF A. Are at decreased risk for ototoxicity from aminoglycoside therapy B. Have few family psychosocial concerns C. Have limited access to highly effective modulator therapy in 2021 D. Rarely have elevated hepatic transaminases 7. Women and men with CF prefer to have discussions about becoming parents A. During adolescence B. At the time of transition to adult care C. Only if decide they want to have children D. Only with fertility and obstetrical specialists 8. Women and men with CF report sexual dysfunction rates in the range of A. 10-20% B. 21-30% C. 31-40% D. > 40% 9: Noninvasive ventilation in CF A. Eliminates the need for other airway clearance techniques B. Reduces nocturnal hypercapnia C. Should be reserved for use as a bridge to transplant D. Does not improve blood gases more than supplemental oxygen alone How much do you agree with the following statements: (1 = Strongly Disagree, 5= Strongly Agree)The supplement enhanced my knowledge on the subject. 1) Strongly disagree 2) Somewhat disagree 3) Neither agree or disagree 4) Somewhat agree 5) Strongly agree The supplement was relevant to my practice. 1) Strongly disagree 2) Somewhat disagree 3) Neither agree or disagree 4) Somewhat agree 5) Strongly agree The overall quality of the articles in the supplement were satisfactory. 1) Strongly disagree 2) Somewhat disagree 3) Neither agree or disagree 4) Somewhat agree 5) Strongly agree Do you have any general comments or recommendations for future topics to be covered in future editions of this supplement series?What behavioral changes do you expect to make in your own practice based on reading the articles in this supplement?CommentsThis field is for validation purposes and should be left unchanged.
